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21st European Congress of Pathology
Istanbul, Turkey, September 08-13, 2007
http://www.ecp2007istanbul.org/
Slide Seminar 10, September 12th
Benign Hematopoetic Proliferations Mimicking Malignancies and Borderline Lymphoproliferative Lesions
Chairpersons: P. Kurtin, İ. Kuzu |
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Return to seminar page |
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Case 2
Presented by: Philippe Gaulard
Clinical History
A 14 year-old boy, originating from Marrocco, was admitted for massive splenomegaly without hepatomegaly. Physical examination disclosed micro-polyadenopathies which were already present 2 years before (To note, a lymph node biopsy performed at that time had been interpreted as showing non specific changes with follicular and paracortical hyperplasia). WBC count was normal except for mild thrombocytosis. Other investigations disclosed IgA deficiency and deficiency in X factor. The mother had a past history of idiopathic thrombocytopenia.
A splenectomy was performed: the spleen weighted 1650 g, was congestive without gross lesions. The images are from the spleen .
Five months after splenectomy, the patient developped severe acute hepatitis which was treated by steroids. Three years after, the patient is well with persistent mild peripheral adenopathies.
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AUTOIMMUNE LYMPHOPROLIFERATIVE SYNDROME (ALPS)
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28.12.2007 |
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